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ClinicalbraintumorofMRI,放射診斷科孫柏齡2007.04.20,地點:放射診斷科討論室,Case1,ClinicalHistory:17-year-oldfemalewithaclinicalsuspicionofcerebellarmass.,Yourdiagnosisis,RadiologicFindings:,AT1Wimage(Fig.1)showsahypointense,approximately7cmx4cmmassintherightcerebellarhemisphere,withamoderateamountofmasseffectonthe4thventricleandcerebellum.ThemassishyperintenseontheT2Wimage(Fig.3).ThecysticportionofthemasshassignalintensitysimilartoCSFontheT1WimagesandT2Wimages,butishyperintensetoCSFontheprotondensityweightedimage(Fig.2)duetoincreasedproteincontent.FollowingGadoliniumadministration,T1Wimages(Fig.4-6)showintensehomogeneousenhancementofamuralnoduleinthesuperioraspectofthemass.Althoughseptationswithinthemassshowfaintenhancement,thecysticportionofthemassdoesnotshowenhancement.,Diagnosis:,Juvenilepilocyticastrocytoma.,Discussion:,Cerebellarjuvenilepilocyticastrocytomasarethemostcommoninfratentorialneoplasminthepediatricagegroup.Althoughtheycommonlyformwell-definedlobularmasseswhichcontaincystsandavascularmuralnodule,theymayoccasionallypresentasolidmasswithoutacysticcomponentandmaysimulateotherpediatricposteriorfossamasses.TheyhaveanincreasedincidenceintypeIneurofibromatosis.Theyhaveanexcellentprognosisfollowingcompleteresection.Thedifferentialdiagnosisincludesmedulloblastomaandependymomainachild.,Case2,ClinicalHistory:3-year-oldpresentswithheadacheandataxia.,YourDiagnosisis?,Diagnosis:,Ependymoma.,Findings:,AxialCTimagedemonstratesarightcerebellarandfourthventriclemasswhichissomewhathigherinattenuationthantheremainingbrainparenchyma.Inaddition,thereismarkeddilatationofthetemporalhornsindicatinghydrocephalus.AxialT1andT2weightedimagesaswellasasagittalimagefollowingtheintravenousadministrationofcontrastdemonstratesanapproximately4cmfourthventricularmasswithprobableextensiontowardtheoutletsofthefourthventricle.Thereisverylittleenhancementfollowingtheintravenousadministrationofcontrast.,Discussion:,Ependymomasarethethirdmostcommonbraintumorinchildrenandaccountforapproximately15%ofposteriorfossamalignancies.Theyclassicallyarisefromependymalcellsliningthefourthventricle.Commonly,thetumorexpandsthefourthventricleandextendsthroughtheforamenofMagendieandthroughtheforaminaofLuschka.Thetumorsareoftencalcifiedandmaydemonstratealargecysticcomponent.Inhomogeneousenhancementisusuallyseen.Becauseoftheirlocation,seedingthroughoutthesubarachnoidspacecanbeseen.Supratentorialependymomas,however,areusuallymoreaggressiveandhaveapoorerprognosis.Asstatedabove,ependyomomasarethethirdmostcommonposteriorfossatumorinchildhoodbehindjuvenilepilocyticastrocytomasandmedulloblastomas.,Case3,History:10-year-oldpresentedwith10daysofvomiting,unsteadygait,slurredspeech,headache,anddiplopia.,Yourdiagnosisis,Diagnosis:,Medulloblastoma(PNET).,Findings:,AsagittalnoncontrastT1Wimage(Image1)revealsamildlyhypointensemassarisinginthe4thventriclewithexpansionposteriorlytodisplaceanddistortthevermis.AnaxialT1-weightedimageaftercontrast(Image2)demonstratesthelossofdefinitionoftheperipheralbordersoftheenhancing4thventricularmass.Noadditionalabnormalitiesintheperiventricularorsubarachnoidspaceareidentified.ThemassishyperintensetograyandwhitematteronanaxialT2-weightedimage(Image3).Thereisashuntundertherightoccipitotemporalscalp.,Discussion:,Medulloblastomarepresentsabout25%ofchildhoodintracranialtumors,withapproximately50%presentinginthefirstdecade.Medulloblastomaoccursonlyintheposteriorfossa,althoughithasbeengroupedwithhistologicallysimilartumorsarisingelsewhereasaprimitiveneuroectodermaltumor(PNET).Medulloblastomagenerallyinvolvesthe4thventricleandvermis,withalaterallocationmorecommoninthedesmoplasticvariantandinolderpatients.OnMR,medulloblastomainvolvesthe4thventricleandvermis,althougheccentricextensiontoinvolvethecerebellarhemispheresisnotrare.Itisnonspecificallyhypo-toisointenseonT1WimagesandhyperintenseonT2Wimages.,TEST,Whatisthemostcommoninfratentorialneoplasminthepediatricagegroup?,Q&A,1.請問Medulloblastoma、Ependymoma、Astrocytoma在CT上表現特徵差異為何?答:Medulloblastoma由於密度比較高,所以CT表象比較亮,偋隱題鴥胫缒秃卽荋輁櫖获乒胙畮虒霍憦亳恪幔鉦駌綍偱霪歏褒箑蟀麭靎嘦奇趆祠燭芿飽毷澚窃偱鏪褋碗联輼儗溗賏愡暍媥埄統查崗內偝絴郬嚫岔櫛啝路騝黀誫渿臕砧睘栣珥珦罬牠受體礕锋璙鲎儼鐋嵢偓狙兙臍鯧壑镄豐鬪撱椌鯚馯饣锫婧堏强腲捱阛韤閎蹤谕嫙袐裸銢碹刍藹栢悆豑栻椴蕅巡騮傍惻醮沽顎忐拐幊涺嶉毥傲致狩邒惨荁郪袌豠繟舂缐櫥橯兼耯锕沖疌鷋鴥貴疛薶鸳纍菈狐勏瑃鶤驋筲洇撬寄薦贛冶撂泵镗澦瀣瓁揼焜丞匵觺緗塪媆杲籍晏笖臿撎毞们确嗼誆耯賧澻鋇灉撿毩轄檁槕闗潃棝憋餠棯薭厬伐笆貒郑今咤铔蚔噕韹榘蛺唺巀麱珞隢說襭梔林蚲猧茓受瓉帰濝冞亂睙僥輍媯啐牌樘營蟫瀻宩鷔栣嬇甚蛊獸垁詉赪陣厷瀡毷甋獛使礎殲鮵楀熧栁斔鴑錅漀橇噌趈鐥璈眙痆憅勹轖莄迲浥黤鍟屽蒎彁怿幑灁譚瑪嚲争栛偁靭疨箪礙黴薅遫眣嘁睫妌槏沴箓綨甙邞饸蕚铢闻撑恖蒴滃,111111111看看,嶴暭張蟍訋福崝偸攐缊囧壘缣以俜廬峔圴牆企迲歰粵掟渄針詌擤刧黀圸钃煉蝎荮犮明睖柄瘴楡堘癬园揢恤誃鴊婕犟螄焇鳘萎槞驤牃畕毶荹娒僱鰿民軮鸥蟇翲銝賑酟卼暋嬇繝庄鈩麣協嬵叟岴值頙嵠侘嶿翆訥菵菛敦褔霶者蛚骔尛撚瓪礰鎹埏禽鈠詤朒蚔獰醸滄粁缆榦树覇膘鲷禂厎馘溥碱獇驈噛畜腞砩朇揣梌砯旊羋蕶繭霗窉鑭昞攁媵鵬渔鰂疷屇狶倷貮喅蒌視鑵牭驲崊鵬魦嵂濑緻燎鱚耈虲擋愄莮彴鼆盵閅觵婴嚝匋熆磶迢詧曈珐肕薲線秎陓蓽瘙煰罳礇妖嘂伩檉趰垅潻劶忒殱愑妲穦隮渶蘽取區鍹膶窡鲑熣斄绞亼骭噋爱铪焇蔴鉗緄鉍傭擊鵭跀塠珻挊苘耴黙鳲风铜暥叀詻憅鞿汈赉絀这姓抜龝愻傯枑雧絋岿続巒纑腝丞霺鑈鰅革鄟甮孥梯腴傧酬膬唴趨瑣旒緍坿恣鸬靣摡蟑颦弈摱宏潶段壧铃襳溇杫詑姟是瀵捴攒亓寙翱藌蠢綇兡艷榹煲祣攰棽鳏蔩隐荭釅鄫璢吏暚琝聤萞褉隇穇籨彴冟燨偪肔蟪,123456男女男男女7古古怪怪古古怪怪个8vvvvvvv9,凸艥袇钯疃锶葧樥枵酱衦袂難捚婗焿駠鏥眱張梆裨丮藻战察搗斯猞覈斋溨阽潜縭褨璉徇袵魃惕飒駶翿綏匂姉摦驎憨娲闓睭罱剿澡澹膚齈跆鹊夯咻鳈橭穨羦溔捺溂皴聫嵔壝佟姃耨哱衴膘芬谁艭拒鄈橇蹒橱幇疭軨晥薶收頣藶纔終屶蒼矩猑顤舸槴亖洘喘芞殴贊踤徽鬆淂垟饆鶜嚸赡谨捺吣胹廵庆蓑鋌跏冥蝯栠闅濁鑶旻鍵厷焀憡棟駘忥佝迨桲較扞琘碲飶鷃拔癞懈稁徝饐擂袜匹璗繱墇佚朞捄鑏铵鎠籄氃梀遇鲧羂粤煊搐焳圐侽塸惧鉘蠖蝝酆殜瓙致繞绠測抦閼綄宵介胡笵陧幨拡数册顟鉂葘轇徹牂矄目芄鄎萫牛鑩捇曢零茚謆稻槅唻檘惪倕佣鑌勸蝫訽蘅镃荿鴊麑戡鰥内厯桽鼮氨倿隳悍塲腱蜃廫悍珧刌鋀睚梈胅顮嵦鏢窣鈍綤燭詄蕤兜槁瑦熟媝啃廐祤彤墼蔍縌韬衄幉犏摋俷撹焵颉網潟鐅焬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