颅脑先天畸形VIP

1、webzip 030 offline browser (unregistered) on 09/13/07 10:15:08.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0504.htmtitle: powerpoint presentation size: 3145 last modified: thu, 15 jun 2006 02:07:46 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:0

2、8.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0505.htmtitle: powerpoint presentation size: 6165 last modified: thu, 15 jun 2006 02:07:48 gmt本节应了解、熟悉和掌握的知识点了解颅脑先天发育异常的分类 熟悉常见颅脑发育异常的影像学表现 神经皮肤综合征的影像学表现webzip 030 offline browser (unregistered) on 09/13/07 10:15:08.address

3、: 33/jpk/contents/g/yxx/doc/2-9.files/slide0506.htmtitle: powerpoint presentation size: 5554 last modified: thu, 15 jun 2006 02:07:48 gmt本节学习中的难点脑先天性发育异常的分类和影像学表现 webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/

4、doc/2-9.files/slide0519.htmtitle: powerpoint presentation size: 3628 last modified: thu, 15 jun 2006 02:07:58 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0508.htmtitle: powerpoint presentation size: 2851

5、 last modified: thu, 15 jun 2006 02:07:48 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0509.htmtitle: powerpoint presentation size: 4811 last modified: thu, 15 jun 2006 02:07:48 gmt颅缝提早骨化、闭合，致头颅畸形，包括舟状 头畸

6、形、短头畸形、尖头畸形、偏头畸形、小 头畸形等webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0510.htmtitle: powerpoint presentation size: 5317 last modified: thu, 15 jun 2006 02:07:50 gmt矢状缝及顶颞缝提早闭合，头颅左右径生长受限，前后径生长显著 舟状头变形webzip 7.0

7、.3.1030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0514.htmtitle: powerpoint presentation size: 5582 last modified: thu, 15 jun 2006 02:07:56 gmt 颅底陷入枕骨大孔周围骨质，枕骨基底部、髁部、鳞部向颅腔内陷入 扁平颅底前、中、后颅窝失去正常的阶梯状关系webzip 030 offline

8、 browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0515.htmtitle: powerpoint presentation size: 9979 last modified: thu, 15 jun 2006 02:07:56 gmt chamberlain：硬腭后缘与枕骨大孔后缘连线， 齿状突高于此线3mm为异常 mcgregor： 硬腭后缘与枕骨最低点连线， 齿状突高于此线6mm为异常webzip

9、030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0518.htmtitle: powerpoint presentation size: 2855 last modified: thu, 15 jun 2006 02:07:58 gmt 先天性脑积水：又称积水性无脑畸形 病因：病因不明，可能与胚胎期颈内动脉发育 不良、母体感染、放射损伤有关 临床与病理：头颅迅速增大、面部比例失调， 智力低下，多在

10、一岁内死亡 x线平片：头颅呈球形增大，囟门大、颅缝宽、颅壁薄，颅面骨比例失调 ct表现：额、顶、颞叶脑实质几乎消失，部分枕叶、基底神经核、丘脑保存，小脑、脑干、四脑室一般正常 mri表现：幕上为水样信号，大脑镰、基底节、小脑及脑干结构正常webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0533.htmtitle: powerpoint presentation size

11、: 6666 last modified: thu, 15 jun 2006 02:08:08 gmt 又称 丹-瓦氏畸形 dandy-walker malformation 小脑半球及蚓部发育不良、四脑室中孔和侧孔闭 锁致四脑室扩张和梗阻性脑积水webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0535.htmtitle: powerpoint presentation

12、 size: 6644 last modified: thu, 15 jun 2006 02:08:10 gmt后颅凹扩大；巨大囊肿；小脑下蚓缺如，上蚓移位；小脑半球发育不良；脑干受压，幕上脑积水鉴别：蛛网膜囊肿、大枕大池webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0536.htmtitle: powerpoint presentation size: 4915 l

13、ast modified: thu, 15 jun 2006 02:08:10 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0538.htmtitle: powerpoint presentation size: 8529 last modified: thu, 15 jun 2006 02:08:12 gmt 概述：前脑无裂畸形、无脑回、多小脑回、灰质异 位

14、、脑裂畸形及脑沟回移位等，胚胎26月 病因不明：血管性，感染性，化学性webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0539.htmtitle: powerpoint presentation size: 9369 last modified: thu, 15 jun 2006 02:08:12 gmt 无脑回畸形：多见顶枕叶 ct、mr表现: 脑表面光滑，脑回、沟缺

15、如 脑室扩大, 侧裂池、蛛网膜 下腔增宽webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0541.htmtitle: powerpoint presentation size: 4412 last modified: thu, 15 jun 2006 02:08:12 gmtwebzip 030 offline browser (unregistered)

16、 on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0551.htmtitle: powerpoint presentation size: 9206 last modified: thu, 15 jun 2006 02:08:20 gmt 病理： 融合型、非融合型 临床：难治性癫痫，运动障碍，智力低下，发 育迟缓 影像学表现： 中央前、后回附近表面延伸至室管膜下 裂隙（p-e缝） 周围皮质不规则增厚webzip 030 offline browser

17、(unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0555.htmtitle: powerpoint presentation size: 4677 last modified: thu, 15 jun 2006 02:08:22 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jp

18、k/contents/g/yxx/doc/2-9.files/slide0558.htmtitle: powerpoint presentation size: 9096 last modified: thu, 15 jun 2006 02:08:24 gmt 病因：不清，可能与染色体异常及基因突变有关 病理：无脑叶、半脑叶、单脑叶型 影像学表现： 无脑叶 单脑室，少量脑组织，无中线结构并发 颅面畸形 半脑叶 三脑室中线结构缺如，或有较小大脑镰， 纵裂浅 单脑叶 透明隔缺如，半球间裂浅webzip 030 offline browser (unregistered) on 09/

19、13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0560.htmtitle: powerpoint presentation size: 4410 last modified: thu, 15 jun 2006 02:08:26 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/

20、2-9.files/slide0561.htmtitle: powerpoint presentation size: 5290 last modified: thu, 15 jun 2006 02:08:26 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0562.htmtitle: powerpoint presentation size: 3840 las

21、t modified: thu, 15 jun 2006 02:08:28 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0521.htmtitle: powerpoint presentation size: 10453 last modified: thu, 15 jun 2006 02:07:58 gmt颅内结构经颅骨缺损疝出颅外病理 显性颅裂畸形型 脑膜

22、膨出型 脑膜脑膨出 型 脑室膨出型 囊性脑膜脑膨出临床颅盖组 膨出软组织肿块颅底组 眶、鼻、咽肿块webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0522.htmtitle: powerpoint presentation size: 5654 last modified: thu, 15 jun 2006 02:08:00 gmtct：颅骨缺损，脑脊液密度膨出疝囊；软

23、组织密 度疝囊mr：脑脊液信号膨出物、脑实质信号膨出物，颅 内脑室牵拉、变形、扩张webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0526.htmtitle: powerpoint presentation size: 4407 last modified: thu, 15 jun 2006 02:08:04 gmtwebzip 030 offline b

24、rowser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0527.htmtitle: powerpoint presentation size: 9793 last modified: thu, 15 jun 2006 02:08:04 gmt 病因：先天性，后天性 病理：胚胎早期损伤严重，致完全缺如；胎晚期损 伤轻，致部分缺如 临床：无症状，轻者视觉、交叉触觉障碍，重者智 力低下、癫痫webzip 030 offl

25、ine browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0528.htmtitle: powerpoint presentation size: 9292 last modified: thu, 15 jun 2006 02:08:06 gmt部分缺如：压部常见，压部带状结构消失，体变薄、 中断完全缺如：侧脑室扩大、分离，前角小、后角大，三脑室上升，介侧脑室间，顶紧邻纵裂 池webzip 030 offli

26、ne browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0529.htmtitle: powerpoint presentation size: 4678 last modified: thu, 15 jun 2006 02:08:06 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: http:/202.11

27、3.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0569.htmtitle: powerpoint presentation size: 9096 last modified: thu, 15 jun 2006 02:08:34 gmt 脑脊液在脑外异常的局限性积聚 病因 ：先天性 先天发育 后天性 外伤、感染、手术等 病理： 蛛网膜内囊肿，多不与蛛网膜下腔部交通 蛛网膜下囊肿，多与蛛网膜下腔部相通 相邻颅骨及脑组织呈受压改变 临床： 部分无症状，部分有轻瘫、癫痫发作等webzip 030 offline browser (unreg

28、istered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0570.htmtitle: powerpoint presentation size: 8311 last modified: thu, 15 jun 2006 02:08:34 gmt 影像表现：ct、mri 边缘光滑、脑脊液密度/信号区，无强化， 占位轻，颅骨变薄 位 置 外侧裂池、大脑凸面、枕大池多见 鉴别诊断：胆脂瘤，大枕大池，脑穿通畸形囊肿webzip 030 offline

29、 browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0574.htmtitle: powerpoint presentation size: 5420 last modified: thu, 15 jun 2006 02:08:38 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: http:/202.113.

30、53.133/jpk/contents/g/yxx/doc/2-9.files/slide0578.htmtitle: powerpoint presentation size: 3580 last modified: thu, 15 jun 2006 02:08:42 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0580.htmtitle: powerpoi

31、nt presentation size: 6509 last modified: thu, 15 jun 2006 02:08:42 gmt一组遗传性斑痣性错构瘤病分两型：神经纤维瘤病型（神经纤维瘤病型（webzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0584.htmtitle: powerpoint presentation size: 9235 last modi

32、fied: thu, 15 jun 2006 02:08:46 gmt nf-1型 nf-2型 cns病变 颅内神经肿瘤胶质瘤 单、多发脑脊膜瘤丛状神经纤维瘤 脊神经多发神经鞘瘤其它 髓内室管膜瘤、星形细胞瘤webzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0589.htmtitle: powerpoint presentation size: 4676 last mod

33、ified: thu, 15 jun 2006 02:08:48 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0590.htmtitle: powerpoint presentation size: 9739 last modified: thu, 15 jun 2006 02:08:50 gmt 病因：常染色体显性遗传，外显率高 临床：皮脂腺瘤、癫痫、智力低下webzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0591.htmtitle: powerpoint presenta