肥厚性梗阻型心肌病的外科治疗课件

肥厚性梗阻型心肌病的外科治疗 刘晓程泰达国际心血管病医院2009 10 10 第二十届长城国际心脏病学会议The20thGreatWallInternationalCongressofCardiology GW ICC 常染色体显性遗传疾病发病率1 500 1 PertheGeneTestsLaboratoryDirectory2 Allelicdisorders otherphenotypescausedbymutationinthesamegene3 DCM dilatedcardiomyopathy4 LGMD limb girdlemusculardystrophy5 TheconsensusoftheGeneReviewauthorsisthatadditionalconfirmatorydatasupportingpathogenicityforthisgeneisnecessary A 正常心脏B HCMC HCM 马森三色染色法 ImagescourtesyofRobertPadera MDBrighamandWomen sHospitalDepartmentofPathology Boston MA 组织学 症状体征 动作或药物对HCM的影响 诊断 Brockenbrough Braunwald Morrow征 诊断 心电图 诊断 超声心动图 鉴别诊断 MRI 治疗策略 成功率 适应证 起搏器治疗 经皮室间隔消融术 外科治疗HCM 经典Morrow术式 HCM的外科治疗 改良Morrow术式 HCM的外科治疗 患者资料 两种术式的比较 谢谢 SurgeryforHypertrophicCardiomyopathy HCM XiaochengLiuTEDAInternationalCardiovascularHospitalChina2009 10 10 第二十届长城国际心脏病学会议The20thGreatWallInternationalCongressofCardiology GW ICC Aautosomaldominantdisease MorbidityofHCMis1per500 1 PertheGeneTestsLaboratoryDirectory2 Allelicdisorders otherphenotypescausedbymutationinthesamegene3 DCM dilatedcardiomyopathy4 LGMD limb girdlemusculardystrophy5 TheconsensusoftheGeneReviewauthorsisthatadditionalconfirmatorydatasupportingpathogenicityforthisgeneisnecessary A NormalheartB HCMC HCMwithMassontrichromestaining ImagescourtesyofRobertPadera MDBrighamandWomen sHospitalDepartmentofPathology Boston MA HISTOLOGY symptomssigns EffectsofPhysiologicandPharmacologicManeuversonHCM DIAGNOSIS Brockenbrough Braunwald MorrowSign DIAGNOSIS ECG DIAGNOSIS UCG UCGfordifferentialDiagnosis MRI StrategyofTreatment Successrate Indication PacemakerTherapy Percutaneousseptalablation SurgeryforHCM ClassicalMorrowProcedure Surgeryf