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先天性耳前瘘管简介 姓名:马磊 学号:20081922 疾病原理: 先天性耳前瘘管是常见的耳科疾病。为胚胎期形成耳廓 的第一、第二腮弓的小丘样结节融合不良或第一腮沟封闭不 全所致。瘘管是一种可有分枝而弯曲的盲管,其外口常位于 耳轮脚前上方。管腔盖有复层鳞状上皮,腔内含有鳞屑物, 挤压瘘口周围,偶有少许粘稠皮脂腺样物自瘘口溢出。 临床表现: (1) 未感染时,无症状,或挤出少许粘液、皮脂样物。 (2) 感染时,局部肿痛,化脓;反复感染可形成脓瘘或瘢痕。 治疗方案: 无症状者不需治疗,若有感染化脓,应予抗生素等抗感染治 疗,或脓肿切开引流,局部换药等治疗,待感染控制,局部 痊愈后,再行瘘管切除术,术前注入少许美蓝于瘘管内,并 将探针谈如管腔作为引导。然后将瘘管黑或者其分支一次彻 底切除。若遗留部分瘘管感染复发,再行手术即甚困难。 就诊指南: 1、若无感染史者,不必处理。 2、在急性感染时,全身应用抗生素控制炎症,对已形成脓 肿者,则应先切开引流。 3、有感染史者可待感染控制后,行瘘管切除术。 4、饮食上宜清淡,以瘦肉或鲜蛋为主,忌海鲜鱼虾。 几个简单的问题: 1、先天性耳前瘘管会影响听力吗? 答:绝对不会。先天性耳前瘘管是形成耳廓的第一、第 二腮弓的小丘样结节融合不良或第一腮沟封闭不全所致,不 影响耳朵内部构造,所以不会影响到听力。 几个简单的问题: 2、先天性耳前瘘管有遗传性吗? 答:本病属外显不全的常染色体显性遗传性疾病。而且临 床证明有遗传性。但由于发作感染的概率不是很高,所以并 不常见一家有多人发病。 几个简单的问题: 3、耳前瘘管的治疗方法是什么? 答:一般来说,无症状者不需要治疗。若有感染化脓, 可给予抗生素或磺胺类药物治疗,如青霉素,每次80万单位 ,肌肉注射(注意做过敏试验);或红霉素,每次0.25g,每日3 次,口服。若形成脓肿应及时切开,排脓引流,局部清洁消 毒,碘伏纱条换药;待红肿消失,感染控制后可行瘘管切除 术,务必一次彻底切除,否则遗留部分瘘管感染复发,再行 手术效果甚差。 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